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Genetic and Rare Diseases Information Center (GARD)

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Amyopathic dermatomyositis


Other Names for this Disease

  • ADM
  • Dermatomyositis sine myositis
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Overview

Amyopathic dermatomyositis is a form of dermatomyositis characterized by the presence of typical skin findings without muscle weakness.[1][2] Some of the skin changes that suggest dermatomyositis include a pink rash on the face, neck, forearms and upper chest; Gottron's papules and heliotrope eyelids.[2][3][4] Pruritis and photosensitivity are common, as is scalp inflammation and thinning of the hair.[2][3] While patients with amyopathic dermatomyositis should not have clinically evident muscle weakness, minor muscle abnormalities may be included. Fatigue is reported in at least 50% of patients.[2] Some cases have been associated with internal malignancy and/or interstitial lung disease.[5] Treatment may include sun avoidance, ample use of sunscreen, topical corticosteroids, antimalarial agents, methotrexate, mycophenolate mofetil, or intravenous (IV) immunoglobulin.[1]
Last updated: 1/10/2013

References

  1. Callen JP. Dermatomyositis. Medscape Reference. October 2011; http://emedicine.medscape.com/article/332783-overview. Accessed 1/10/2013.
  2. Olsen NJ, Park JH, King LE Jr. Amyopathic dermatomyositis. Curr Rheumatol Rep. Aug 2001; http://www.ncbi.nlm.nih.gov/pubmed/11470054. Accessed 1/10/2012.
  3. Dermatomyositis. DermNet NZ. 2011; http://www.dermnetnz.org/immune/dermatomyositis.html. Accessed 1/10/2013.
  4. Saoud B, Allali F, Hassouni NH. Amyopathic dermatomyositis. Joint Bone Spine. May 2006; http://www.ncbi.nlm.nih.gov/pubmed/16253536. Accessed 1/10/2013.
  5. Sato S, Kuwana M. Clinically amyopathic dermatomyositis. Curr Opin Rheumatol. Nov 2010; http://www.ncbi.nlm.nih.gov/pubmed/20827200. Accessed 1/10/2013.
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Basic Information

  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • Orphanet is a European reference portal for¬†information on rare diseases and orphan drugs.¬† Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Amyopathic dermatomyositis. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • ADM
  • Dermatomyositis sine myositis
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.