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Pityriasis lichenoides et varioliformis acuta

Other Names for this Disease
  • Mucha-Habermann disease
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What causes pityriasis lichenoides et varioliformis acuta (PLEVA)?

The exact cause of pityriasis lichenoides et varioliformis acuta (PLEVA) is unknown.[1][2][3]  However, three major theories regarding the cause have been proposed. These include:[1]

  • An inflammatory reaction triggered by infectious agents
  • A relatively benign form of T-cell lymphoproliferative disorder
  • An immune-complex-mediated hypersensitivity vasculitis

Some of the infections that have been associated with PLEVA include:[1][2]

Last updated: 1/3/2012

  1. Pityriasis lichenoides. New Zealand Dermatological Society Web site. 2011; Accessed 1/3/2012.
  2. Klein PA. Pityriasis Lichenoides. eMedicine. July 2010; Accessed 1/3/2012.
  3. Paller AS. Mucha Habermann Disease. National Organization for Rare Disorders (NORD). 2009; Accessed 1/3/2012.