Your browser does not support javascript:   Search for gard hereSearch for news-and-events here.


Genetic and Rare Diseases Information Center (GARD)

Print friendly version

Pityriasis lichenoides et varioliformis acuta

Other Names for this Disease
  • Mucha-Habermann disease
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.


Pityriasis lichenoides et varioliformis acuta (PLEVA) is a rare skin disorder that is characterized as a more severe form of pityriasis lichenoides. Signs and symptoms usually begin with itchy, burning skin lesions that ulcerate, breakdown, form open sores, then form a red-brown crust. Individuals with PLEVA may also experience a low-grade fever, headache, malaise (a vague feeling of bodily discomfort), and arthralgias (severe joint pain); these symptoms may occasionally precede or accompany the skin findings. The underlying cause of pityriasis lichenoides and PLEVA is unknown. Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe form of PLEVA.[1][2]
Last updated: 1/3/2012


  1. Ersoy-Evans S, Fernanda Greco M, Mancini AJ, Subasi N, Paller AS.  Pityriasis lichenoides in childhood: A retrospective review of 124 patients.  J Am Acad Dermatol. Feb 2007; 56(2): 205-210.
  2. Bowers S, Warshaw EM.  Pityriasis lichenoides and its subtypes.  J Am Acad Dermatol. Oct 2006; 55(4): 557-572.
Your Questions Answered
by the Genetic and Rare Diseases Information Center

5 question(s) from the public on Pityriasis lichenoides et varioliformis acuta have been answered. See questions and answers. You can also submit a new question.

Basic Information

  • The British Association of Dermatologists provides an informational leaflet on pityriasis lichenoides.  Click on the British Association of Dermatologists link to view this leaflet.
  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Pityriasis lichenoides et varioliformis acuta. Click on the link to view a sample search on this topic.

Resources for Kids

  • Kids Skin Health, a American Academy of Dermatology's web site, provides kids, teens, and parents with information on skin conditions. Click on Kids Skin Health to access this Web site.