Pityriasis lichenoides et varioliformis acuta
Other Names for this Disease
- Mucha-Habermann disease
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Your QuestionWhat is the incidence of pityriasis lichenoides et varioliformis acuta (PLEVA) in the United States? How often does PLEVA turn into something more serious?
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The incidence of PLEVA in the United States has not been reported.
Last updated: 8/6/2010
Occasional cases (<2%) of PLEVA have been reported to evolve into cutaneous lymphoma. Rarely, a severe variant of PLEVA called febrile ulceronecrotic Mucha-Habermann disease (FUMHD) develops. FUMHD often begins as PLEVA, but then rapidly and suddenly progresses to large, destructive ulcers. There may be fever and extensive, painful loss of skin tissue as well as secondary infection of the ulcers. Patients may develop complications such as interstitial pneumonitis, abdominal pain, malabsorption, central nervous system involvement, bacteremia, sepsis, and rheumatic manifestations.
Last updated: 10/22/2010
- Klein PA, Callen JP. Pityriasis Lichenoides. eMedicine. 2010; http://emedicine.medscape.com/article/1099078-overview. Accessed 8/6/2010.