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Genetic and Rare Diseases Information Center (GARD)

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Pityriasis lichenoides et varioliformis acuta


Other Names for this Disease
  • Mucha-Habermann disease
  • PLEVA
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Overview


Pityriasis lichenoides et varioliformis acuta (PLEVA) is a rare skin disorder that is characterized as a more severe form of pityriasis lichenoides. Signs and symptoms usually begin with itchy, burning skin lesions that ulcerate, breakdown, form open sores, then form a red-brown crust. Individuals with PLEVA may also experience a low-grade fever, headache, malaise (a vague feeling of bodily discomfort), and arthralgias (severe joint pain); these symptoms may occasionally precede or accompany the skin findings. The underlying cause of pityriasis lichenoides and PLEVA is unknown. Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare and severe form of PLEVA.[1][2]
Last updated: 1/3/2012

References

  1. Ersoy-Evans S, Fernanda Greco M, Mancini AJ, Subasi N, Paller AS.  Pityriasis lichenoides in childhood: A retrospective review of 124 patients.  J Am Acad Dermatol. Feb 2007; 56(2): 205-210. http://www.ncbi.nlm.nih.gov/pubmed/17097385.
  2. Bowers S, Warshaw EM.  Pityriasis lichenoides and its subtypes.  J Am Acad Dermatol. Oct 2006; 55(4): 557-572. http://www.ncbi.nlm.nih.gov/pubmed/17010734.
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Basic Information

  • The British Association of Dermatologists provides an informational leaflet on pityriasis lichenoides.  Click on the British Association of Dermatologists link to view this leaflet.
  • DermNet NZ is an online resource about skin diseases developed by the New Zealand Dermatological Society Incorporated. DermNet NZ provides information about this condition.
  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • Medscape Reference provides information on this topic. Click on the link to view this information. You may need to register to view the medical textbook, but registration is free.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Pityriasis lichenoides et varioliformis acuta. Click on the link to view a sample search on this topic.

Resources for Kids

  • Kids Skin Health, a American Academy of Dermatology's web site, provides kids, teens, and parents with information on skin conditions. Click on Kids Skin Health to access this Web site.