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Genetic and Rare Diseases Information Center (GARD)

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Chiari malformation type 1


* Not a rare disease
Other Names for this Disease
  • Arnold Chiari malformation type I
  • Chiari malformation type I
  • Chiari type I malformation
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Chiari malformation type 1 is a structural abnormality of the cerebellum, the part of the brain that controls balance. It involves the extension of the lower part of the cerebellum into the foramen magnum (the large hole at the base of the skull which allows passage of the spinal cord), without involving the brainstem. Normally, only the spinal cord passes through this opening. This malformation is the most common type of Chiari malformation and may not cause any symptoms.[1] Depending on the symptoms present and severity, some individuals may not require treatment while others may require pain medications or surgery.[2][3]
Last updated: 3/12/2012


  1. Chiari Malformation Fact Sheet. National Institute of Neurological Disorders and Stroke Web site. 2009; Accessed 12/22/2009.
  2. Chiari Malformation Fact Sheet. NINDS. February 1, 2012; Accessed 3/11/2012.
  3. Peyman Pakzaban. Chiari Malformation. eMedicine. March 2, 2012; Accessed 3/11/2012.
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