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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Scleromyxedema


Other Names for this Disease

  • Arndt-Gottron disease
  • Generalized lichenoid papular eruption
  • Generalized papular and sclerodermoid
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Treatment

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How might scleromyxedema be treated?

There is no standard treatment for scleromyxedema. The severe course of the disease requires very aggressive treatment, and long-term maintenance therapy is usually necessary. According to the literature, the use of intravenous immunoglobilin (IVIG) may be successful; this type of treatment can have relatively long-term effects and few side effects. Because of this, it is currently considered the best treatment option. Plasmapheresis is effective as a short-term treatment and leads to relapses (recurrence of symptoms).[1]
Last updated: 4/18/2014

References
  1. Koronowska SK, Osmola-Mankowska A, Jakubowicz O, Zaba R. Scleromyxedema: a rare disorder and its treatment difficulties. Postepy Dermatol Alergol. April, 2013; 30(2):122-126. Accessed 4/18/2014.


Other Names for this Disease
  • Arndt-Gottron disease
  • Generalized lichenoid papular eruption
  • Generalized papular and sclerodermoid
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.