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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Nevoid basal cell carcinoma syndrome


Other Names for this Disease

  • Basal Cell Nevus Syndrome
  • Fifth Phacomatosis
  • Gorlin Syndrome
  • Gorlin-Goltz Syndrome
  • Multiple Basal Cell Nevi, Odontogenic Keratocysts, And Skeletal Anomalies
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Prognosis

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What is the long-term outlook for people with nevoid basal cell carcinoma syndrome?

The life expectancy for people with nevoid basal cell carcinoma syndrome (NBCCS) is not significantly different from people without NBCCS. Although young children often have some delay in motor milestones, most of them catch up by about 5 years of age. The major problem is with the cosmetic effect of treatment of multiple skin tumors and treatment of jaw keratocysts. A poor cosmetic outcome can lead to social difficulties, including difficulty maintaining employment.[1]
Last updated: 7/16/2014

References
  1. D Gareth Evans and Peter A Farndon. Nevoid Basal Cell Carcinoma Syndrome. GeneReviews. March 7, 2013; http://www.ncbi.nlm.nih.gov/books/NBK1151/. Accessed 7/16/2014.


Other Names for this Disease
  • Basal Cell Nevus Syndrome
  • Fifth Phacomatosis
  • Gorlin Syndrome
  • Gorlin-Goltz Syndrome
  • Multiple Basal Cell Nevi, Odontogenic Keratocysts, And Skeletal Anomalies
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.