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Idiopathic pulmonary hemosiderosis

Other Names for this Disease
  • Alveolar hypoventilation syndrome
  • Hemosiderosis, pulmonary, with deficiency of gamma-a globulin
  • Pulmonary hemosiderosis
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Idiopathic pulmonary hemosiderosis is a rare disease characterized by repeated episodes of bleeding into the lungs, which can cause anemia. The body is able to remove most of the blood from the lungs, but a large amount of iron is often left behind. Over time, this iron can cause permanent damage to the lungs. Signs and symptoms usually occur after chronic blood loss or blood in the lungs. Symptoms can include coughing, difficulty breathing, and wheezing, resembling pneumonia. Affected individuals who do not have a large amount of pulmonary bleeding can do well, while others with large amounts of bleeding may only live for a few years. The cause of this condition is currently unknown.[1]
Last updated: 1/29/2013


  1. Idiopathic pulmonary hemosiderosis. Madisons Foundation. 2011; Accessed 1/29/2013.
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  • The Online Mendelian Inheritance in Man (OMIM) is an catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
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