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Hypoplastic left heart syndrome

Other Names for this Disease
  • HLHS
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Hypoplastic left heart syndrome (HLHS) is a problem with the heart’s structure that is present at birth (congenital). It occurs when parts of the left side of the heart (mitral valve, left ventricle, aortic valve, and aorta) do not develop completely.[1] The underdeveloped left side of the heart is unable to provide enough blood flow to the body, which decreases the oxygen-rich blood supply. Babies with HLHS might look normal at birth, but will develop symptoms of HLHS within a few days. These symptoms might include: poor feeding, problems breathing, pounding heart, weak pulse, and ashen or bluish skin color. The cause of HLHs is presently unknown.[2]
Last updated: 7/21/2011


  1. Schumacher KR. Hypoplastic left heart syndrome. MedlinePlus. December 2009; Accessed 7/21/2011.
  2. Facts about Hypoplastic Left Heart Syndrome. Centers for Disease Control and Prevention. April 2011; Accessed 7/21/2011.
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