Dentinogenesis imperfecta 1
Other Names for this Disease
- Capdepont teeth
- Dentinogenesis imperfecta Shields type 2
- Dentinogenesis imperfecta type 1
- Dentinogenesis imperfecta without osteogenesis imperfecta
- Opalescent dentin
Your QuestionI would like to learn more about dentinogenesis imperfecta. How is this condition treated? How can I get in touch with others affected by this condition?
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Questions on this page
Researchers have described three types of dentinogenesis imperfecta with similar dental abnormalities. Type I occurs in people who have osteogenesis imperfecta, a genetic condition in which bones are brittle and easily broken. Dentinogenesis imperfecta type II and type III usually occur in people without other inherited disorders. A few families with type II have progressive hearing loss in addition to dental abnormalities. Type III was first identified in a population in Brandywine, Maryland. Some researchers believe that dentinogenesis imperfecta type II and type III, along with a similar condition called dentin dysplasia type II, are actually forms of a single disorder.
Crowns, caps or other forms of dental care are the most commonly used treatments. Dentures or dental implants may be necessary if the majority of teeth are lost.
More detailed information regarding the treatment of dentinogenesis imperfecta can be found by visiting the following web links:
Osteogenesis Imperfecta Foundation
804 W. Diamond Ave, Suite 210
Gaithersburg, MD 20878
Web site: http://www.oif.org/site/PageServer
Page on dentinogenesis imperfecta: http://www.oif.org/site/PageServer?pagename=Dental
Additional resources may be located through the Support Groups section of the resources page on this topic.
- Dentinogenesis imperfecta. Genetics Home Reference (GHR). November 2009; http://ghr.nlm.nih.gov/condition=dentinogenesisimperfecta. Accessed 4/29/2011.
- Barron MJ, McDonnell ST, MacKie I, Dixon MJ. Hereditary dentine disorders: dentinogenesis imperfecta and dentine dysplasia. Orphanet Journal of Rare Diseases. November 2008; http://www.ojrd.com/content/3/1/31. Accessed 4/29/2011.
- Wulfsberg EA. Dentinogenesis imperfecta. Center for Craniofacial Development and Disorders, Johns Hopkins University. December 29, 2003; http://www.hopkinsmedicine.org/craniofacial/Education/DefinedArticle.cfm?MUArticleID=103&Source=Family. Accessed 5/4/2009.