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Genetic and Rare Diseases Information Center (GARD)

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Arrhythmogenic right ventricular dysplasia

Other Names for this Disease
  • Arrhythmogenic right ventricular cardiomyopathy
  • ARVC
  • ARVD
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What is arrhythmogenic right ventricular dsyplasia?

What is arrhythmogenic right ventricular dsyplasia?

Arrhythmogenic right ventricular dysplasia (ARVD) is an inherited heart condition in which the muscle of the right ventricle of the heart is replaced by fat and/or scar tissue. The condition is progressive and over time the right ventricle loses the ability to pump blood.[1] Individuals with ARVD often develop abnormal heart rhythms known as arrhythmias, which can increase the risk of sudden cardiac arrest or death. Other symptoms of ARVD include chest palpitations, dizziness, fainting and shortness of breath. Often, sudden cardiac death can be the first sign of ARVD. ARVD is caused by genetic mutations in genes that instruct proteins to link one heart cell to the next. There is also some evidence that ARVD could be caused by an infection of the heart muscle. Treatment options can vary by patient and may include anti-arrhythmogenic medication, implantable cardioverter defibrillators and catheter ablation.[2][3]
Last updated: 1/30/2013

  1. Cleveland Clinic. Arrhythmogenic Right Ventricular Dysplasia (ARVD). March 2010; Accessed 1/28/2013.
  2. Johns Hopkins Medicine. Symptoms and Diagnosis. ARVD. Accessed 1/28/2013.
  3. Eric Anderson. Arrhythmogenic Right Ventricular Dysplasia. American Family Physician. April 2006; 8:1391-1398. Accessed 1/28/2013.