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Genetic and Rare Diseases Information Center (GARD)

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Pulmonary sequestration


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Overview

Pulmonary sequestration is a rare malformation where non-functioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation.[1][2] It may be congenital (present from birth) or acquired.[2] Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location.[2][3] Symptoms may include chronic cough, respiratory distress or infection. Treatment depends on the location and may involve surgery.[2]
Last updated: 4/6/2010

References

  1. Pikwer A, Gyllstedt E, Lillo-Gil R, et al.. Scand J Surg. 2006; http://www.ncbi.nlm.nih.gov/pubmed/17066616. Accessed 4/6/2010.
  2. Khan AN, Aird M, Chiphang A, et al.. Pulmonary Sequestration. eMedicine. 2008; http://emedicine.medscape.com/article/412554-overview. Accessed 4/6/2010.
  3. Kliegman. Chapter 392 - Congenital Disorders of the Lung. In: Finder JD, Michelson PH. Nelson Textbook of Pediatrics, 18th ed.. Saunders; 2007;
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In Depth Information

  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Pulmonary sequestration. Click on the link to view a sample search on this topic.
  • eMedicine has two articles on this topic from the perspective of Pediatrics and Radiology. You may need to register to view the information online, but registration is free. Click on the links above to view the articles from this medical reference Web site.
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.