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Becker nevus syndrome

Other Names for this Disease
  • Hairy epidermal nevus syndrome
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Becker nevus syndrome is characterized by the presence of a Becker nevus in association with underdevelopment (hypoplasia) of the breast or other skin-related, muscular, or skeletal defects, all of which usually involve the same side of the body as the nevus (ipsilateral).[1] Specific signs and symptoms in addition to the nevus may include ipsilateral breast hypoplasia; skeletal abnormalities such as hypoplasia of the shoulder girdle, scoliosis, fused ribs, and ipsilateral shortness of the arm; and several other features.[2][1] The condition is thought to be sporadic (occurring in individuals with no history of the condition in the family).[1] Treatment varies depending upon the specific symptoms present and the extent of the condition in the affected individual.[2]
Last updated: 4/25/2012


  1. Wilson H. Y. Lo. Becker Nevus Syndrome. OMIM. May 4, 2000; Accessed 4/23/2012.
  2. Epidermal Nevus Syndromes. NORD. June 20, 2011; Accessed 4/23/2012.
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Basic Information

  • The National Organization for Rare Disorders (NORD) is a federation of more than 130 nonprofit voluntary health organizations serving people with rare disorders. Click on the link to view information on this topic.

In Depth Information

  • The Online Mendelian Inheritance in Man (OMIM) is an catalog of human genes and genetic disorders. Each entry has a summary of related medical articles. It is meant for health care professionals and researchers. OMIM is maintained by Johns Hopkins University School of Medicine. 
  • Orphanet is a European reference portal for information on rare diseases and orphan drugs.  Access to this database is free of charge.
  • PubMed is a searchable database of medical literature and lists journal articles that discuss Becker nevus syndrome. Click on the link to view a sample search on this topic.