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Meningoencephalocele


Other Names for this Disease

  • Encephalomeningocele
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Overview

Meningoencephalocele is a type of encephalocele, which is an abnormal sac of fluid, brain tissue, and meninges (membranes that cover the brain and spinal cord) that extends through a defect in the skull.  There are two main types of meningoencephalocele, which are named according to the location of the sac. The frontoethmoidal type is located at the frontal and ethmoid bones while the occipital type is located at the occipital bone.  Hydrocephalus, abnormalities of the eyeball and tear duct, and other findings have been associated with the condition.[1][2] Some affected individuals have intellectual or physical disabilities while others have normal development and abilities.[3]  The condition is typically congenital (present at birth) but has been reported to develop by chance in older individuals in rare cases.[4] The underlying cause of the condition is uncertain, but environmental factors are thought to play a role. Treatment depends on the size, location and severity of the defect but mainly includes magnetic resonance imaging (MRI) to determine the severity of the defect, followed by surgery to repair it.[1][2]
Last updated: 8/27/2014

References

  1. Sitthiporn Agthong and Viroj Wiwanitkit. Encephalomeningocele cases over 10 years in Thailand: a case series. BMC Neurology. 2002; 2:http://www.ncbi.nlm.nih.gov/pmc/articles/PMC113760/?tool=pubmed. Accessed 9/19/2011.
  2. Kiymaz N, Yilmaz N, Demir I, Keskin S. Prognostic Factors in Patients with Occipital Encephalocele. Pediatric neurosurgery 2010. 2010; 46(1):6-11.
  3. Meling TR, Due-T√łnnessen BJ, Helseth E, Skjelbred P, Arctander K. [Frontoethmoidal meningoencephaloceles]. Tidsskr Nor Laegeforen. August 20, 2000; 120(19):2250-2252.
  4. Nahas Z. Spontaneous meningoencephalocele of the temporal bone: clinical spectrum and presentation. Arch Otolaryngol Head Neck Surg. May 1, 2008; 134(5):509-518.
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In Depth Information

  • PubMed is a searchable database of medical literature and lists journal articles that discuss Meningoencephalocele. Click on the link to view a sample search on this topic.
Other Names for this Disease
  • Encephalomeningocele
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.