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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Jones syndrome


Other Names for this Disease

  • Familial gingival fibromatosis associated with progressive deafness
  • GFD
  • Gingival fibromatosis with progressive deafness
  • Gingival fibromatosis with sensorineural hearing loss
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Treatment

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How might Jones syndrome be treated?

Due to the rarity of Jones syndrome, there are no treatment guidelines available in the medical literature. However, there is information about how the features associated with Jones syndrome might be treated.

Treatment for gingival fibromatosis varies depending on the severity. Maintaining good oral hygiene is very important. Surgery to remove the enlarged gum tissue in the mouth (gingivectomy) may be needed for functional and/or cosmetic reasons. Enlargement may recur to various extents, and repeated surgeries may be needed to reshape the gums. It has been recommended that whenever possible, this treatment should be performed after the complete eruption of permanent teeth.[1]

The goal of treatment for sensorineural hearing loss is to improve hearing. People with sensorineural hearing loss may use hearing aids; telephone amplifiers and other assistive devices; sign language (for those with severe hearing loss); and/or speech reading (such as lip reading and using visual cues to aid communication). A cochlear implant may be recommended for some people with severe hearing loss.[2]
Last updated: 10/7/2014

References
  1. Aghili H, Goldani Moghadam M. Hereditary gingival fibromatosis: a review and a report of a rare case. Case Rep Dent. 2013; Accessed 10/7/2014.
  2. Sensorineural deafness. MedlinePlus. October 2, 2014; http://www.nlm.nih.gov/medlineplus/ency/article/003291.htm. Accessed 10/7/2014.


Other Names for this Disease
  • Familial gingival fibromatosis associated with progressive deafness
  • GFD
  • Gingival fibromatosis with progressive deafness
  • Gingival fibromatosis with sensorineural hearing loss
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.