Your browser does not support javascript:   Search for gard hereSearch for news-and-events here.

Diseases

Genetic and Rare Diseases Information Center (GARD)

Print friendly version

Congenital extrahepatic portosystemic shunt


Other Names for this Disease
  • Abernethy malformation
  • CEPS
See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.

Symptoms


Newline Maker

What are the symptoms of congenital extrahepatic portosystemic shunt?

The symptoms of congenital extrahepatic portosystemic shunt (CEPS) vary and are caused by blood not moving through the liver.  The liver removes certain toxic chemicals from the blood; if a CEPS exists, these chemicals stay in the blood and can cause signs of liver disease or problems in the brain (hepatic encephalopathy).  Hepatic encephalopathy occurs more often in older people with CEPS.[1]
Last updated: 2/1/2012

References
  1. Alonso-Gamarra E, Parrón M, Pérez A, Prieto C, Hierro L, López-Santamaría M. Clinical and radiologic manifestations of congenital extrahepatic portosystemic shunts: a comprehensive review. Radiographics. 2011; 31:707-722. http://www.ncbi.nlm.nih.gov/pubmed/21571652. Accessed 1/27/2012.