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Diseases

Genetic and Rare Diseases Information Center (GARD)

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Epithelioid sarcoma


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Overview

What is epithelioid sarcoma?

What is epithelioid sarcoma?

Epithelioid sarcoma is a rare cancer that most often occurs in the soft tissue of the fingers, hands and forearms of young adults.[1]  It may also be found in the legs, trunk, head or neck regions.  It is rare in young children and adults, and it occurs more frequently in men.[2][3]  Epithelioid sarcoma begins as a painless, firm growth or bump that may be accompanied by an open wound (ulceration) in the skin covering the growth.[3]  It is considered an aggressive cancer because it has a high chance of regrowing after treatment (a recurrence), or spreading to surrounding tissues or more distant parts of the body (a metastasis).[3]  Epithelioid sarcoma is first treated with surgery to remove all the cancer cells (wide local excision).[2][3]  Amputation of part of the affected limb may be needed in severe cases.[1]  Radiation therapy or chemotherapy may also be used to destroy any cancer cells not removed during surgery.[2]
Last updated: 9/16/2011

References
  1. Nagoshi N, Anazawa U, Morioka H, Mukai M, Yabe H, Toyama Y. Epithelioid sarcoma arising on the forearm of a 6-year-old boy: case report and review of the literature. Pediatric Surgery International. 2006; 22:771-773. http://www.ncbi.nlm.nih.gov/pubmed/16786373. Accessed 9/13/2011.
  2. Pai KK, Pai SB, Sripathi H, Pranab, Rao P. Epithelioid sarcoma: a diagnostic challenge. Indian Journal of Dermatology, Venereology and Leprology. 2006; 72:446-448. http://www.ncbi.nlm.nih.gov/pubmed/17179622. Accessed 9/13/2011.
  3. Armah HB, Parwani AV. Epithelioid Sarcoma. Archives of pathology & Laboratory Medicine. 2009; 133:814-819. http://www.ncbi.nlm.nih.gov/pubmed/19415960. Accessed 9/13/2011.


See Disclaimer regarding information on this site. Some links on this page may take you to organizations outside of the National Institutes of Health.